Glutaroyl carnitine Chemische Eigenschaften,Einsatz,Produktion Methoden
Chemische Eigenschaften
Clear Thick Gel
Verwenden
A metabolite of L-Carnitine (C184110).
Biochem/physiol Actions
Increased formation and excretion of glutarylcarnitin results from a glutaryl-CoA dehydrogenase deficiency, an inborn error of lysine and tryptophan metabolism. Secondary carnitine depletion due to increased formation and urinary excretion of glutarylcarnitine is suggested to play an important role in the neuropathogenesis of glutaryl-CoA dehydrogenase deficiency, inducing excitotoxic neuronal damage and mitochondrial dysfunction.
Glutaroyl carnitine Upstream-Materialien And Downstream Produkte
Upstream-Materialien
Downstream Produkte